Dernières publications

Chiffres clés

52 Publications avec texte intégral

Open Access

87 %

Mots clés

Acetylcholine receptor subunit epsilon LRP4 Motor neuron Antisense morpholino Muscular dystrophy Bioinformatics CRISPR/Cas9 Myotube Dystrophin Antisense oligonucleotide RNA interference ICU-acquired weakness Neuromuscular disease Immortalized dystrophic canine myoblast Emerin Human Canine X-linked muscular dystrophy in Japan CXMD J CLS CFTR correctors Expanded repeats Gel electrophoresis Glucocorticoid-induced muscle atrophy Atrial cardiac defects Autophagosome DM1 myoblasts Eteplirsen Exondys 51 Fibroblast DNM2 FSHD Exon-skipping Duchenne muscular dystrophy Neuromuscular junction Becker muscular dystrophy LTβR Adhesion Duchenne Muscular Dystrophy 3D co-culture Gene Therapy Allele-specific silencing Fluorescence microscopy Coculture KLF15 Alternative splicing CTG⋅CAGn repeat Dynamin 2 Clinical trial candidate screening Cell Therapy Human artificial chromosomes Fibrosis BAF Human muscle stem/progenitor cells Bile acid Dominant centronuclear myopathy Endocytosis Developmental biology CXCR4 Drisapersen HDMD/Dmd-null mice Chromatin BMD Gene network analysis Myogenesis Lamin A/C nuclei DiPRO1 CXCL12 Exon Skipping Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS Conjugation ITSN1 Autophagy Flavonoid Insulin Exon skipping FoxO Centronuclear myopathy Genetics Skeletal muscle Gut microbiota Fear response Adeno-associated viral vector Actin Glucose Biomimetism Computer software Migration Folding-defective proteins Immortalisation Cell-penetrating peptide DsDNA break repair Cell biology Gene therapy Myotonic dystrophy DMD Differentiation CDNA synthesis Muscle Culture platform Allele-specific silencing therapy CMS